Paediatric Restrictive Cardiomyopathy - Diagnosis and Challenges

نویسندگان

چکیده

Restrictive cardiomyopathy is one of the rarest forms cardiomyopathies in pediatric patients characterized by impaired myocardial relaxation or compliance with restricted ventricular filling, leading to a reduced diastolic volume preserved systolic function. We report two cases – 5-year-old boy who presented abdominal distension and palpitation family history similar complaints but no definite genetic diagnosis as yet, girl chronic cough shortness breath. Both were diagnosed Sultan Qaboos University Hospital 2019 are managed supportively regular outpatient follow-up. This first series reported restrictive from Oman.
 Keywords: cardiomyopathy, children, heart failure children.

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ژورنال

عنوان ژورنال: Sultan Qaboos University Medical Journal

سال: 2023

ISSN: ['2075-0528', '2075-051X']

DOI: https://doi.org/10.18295/squmj.9.2023.055